Description
Solid pseudopapillary tumours (SPT) of the pancreas are rare (usually benign) pancreatic tumours. They are extremely rare and thought to account for 1-2% of exocrine pancreatic tumours. They tend to present in young non-Caucasian females around the 2nd and 3rd decades of life. Most patients are asymptomatic at diagnosis. They may occasionally present with a gradually enlarging abdominal mass or vague abdominal pain. The tumours frequently contain varying amounts of necrosis, haemorrhage, and cystic change. Lesions can be large at time of diagnosis (median size ~8 cm) 2. The tumour has been referred to with multiple different names, including: solid pseudopapillary tumour (SPT) of the pancreas, solid pseudopapillary neoplasm (SPN), solid pseudopapillary epithelial neoplasm (SPEN), papillary cystic neoplasm of the pancreas, Hamoudi tumour, Gruber-Frantz tumour (or just Frantz tumour)